Pulmonary Fibrosis

Pulmonary fibrosis is deposition of excess fibrous connective tissue in the lungs. It presents as shortness of breath, fatigue, and chronic dry cough. Commonly, it is idiopathic. Other diseases and conditions that predispose to pulmonary fibrosis include hypersensitivity pneumonitis, cigarette smoking, connective tissue diseases, radiation, and medications (e.g. amiodarone, bleomycin, or methotrexate).

Case #1. Pulmonary fibrosis with ground glass opacities and traction bronchiectasis. No definite honeycombing.

Case #2. Pulmonary fibrosis with more limited distribution.

Case #3. Case of idiopathic pulmonary fibrosis: prominent honeycombing seen in right lung field.

Case #4.  Severe idiopathic pulmonary fibrosis with ground glass opacities, traction bronchiectasis, and air cysts.


Case #5. Patient with Erdheim-Chester disease. Cystic interstial lung disease with fibrosis.